Teratologic Hip Dislocations : Controversies and Consensus

Volume 6 | Issue 2 | May-August 2020 | Page: 33-38 | Sukalyan Dey, Prerana Gogoi, Rupjyoti Gogoi, Tofile Ahmed, Roopak Patel, Diganta Phukan


Authors: Sukalyan Dey [1], Prerana Gogoi [2], Rupjyoti Gogoi [3], Tofile Ahmed [4], Roopak Patel [4], Diganta Phukan [4]

[1] Department of Orthopaedics, Fakhruddin Ali Ahmed Medical College, Barpeta, Assam, India.
[2] Resident Medical Officer, Pratiksha Hospital, Guwahati
[3] Consultant Orthopedic Surgeon, Gauhati Neurological Research Center, Six Mile, Guwahati
[4] Department of Orthopaedics, CORAS Pratiksha Hospital, Guwahati.

Address of Correspondence
Dr. Sukalyan Dey,
Department of Orthopaedics, Fakhruddin Ali Ahmed Medical College,
Barpeta, Assam, India.
E-mail: sukalyan.gmch@gmail.com


Abstract

Background: The optimal management for untreated developmental dysplasia of the hip (DDH) after walking age remains controversial.
Methods: We retrospectively reviewed 80 DDH patients (85 hips) diagnosed at one through 3 years of age who underwent gradual reduction (GR) using overhead traction (OHT) with a mean follow-up of 8.2 years. We investigated radiological severity of DDH, successful reduction, avascular necrosis (AVN) of the femoral head, residual dysplasia, secondary procedures, and Severin classification. The data were compared between patients under (42 hips) and over (43 hips) 18 months of age at diagnosis.
Results: Eighty-three hips (98%) were successfully reduced by OHT. Three hips (4%) re-dislocated later and needed closed reduction or open reduction with Salter osteotomy. No AVN occurred during follow-up. Sixty-eight hips were observed without further treatment beyond 5 years of age, of which 52 (76%) remained acetabular dysplasia and 47 (69%) underwent Salter osteotomy with or without femoral osteotomy. We could finally evaluate 69 hips using Severin classification, and 52 (75%) were classified in Group I, 10 (14%) in Group II, and seven (10%) in Group III. Radiological severity of DDH at diagnosis was the only significant variable between the groups: High hip dislocation was more frequently observed in the older age group (p = 0.0131).
Conclusions: GR using OHT is a beneficial initial treatment with a high reduction rate and a low incidence of complications for DDH after walking age, from 1 to 3 years of age. Salter osteotomy performed during preschool ages can provide a satisfactory mid-term outcome for hips with residual acetabular dysplasia after OHT.
Level of Evidence: Therapeutic studies, level IV (case series).
Keywords: Developmental dysplasia of the hip; Walking age; Gradual reduction; Overhead traction; Salter innominate osteotomy.


References 

1. Katz JF. Teratological hip dislocation. Isr J Med Sci 1980;16:238-44.
2. LeBel ME, Gallien R. The surgical treatment of teratologic dislocation of the hip. J Pediatr Orthop B 2005;14:331-6.
3. Aaro S, Gottfries B, Kraepelien T, Troell S. Teratologic congenital dislocation of the hip. Report of two cases. Acta Orthop Scand 1983;54:178-81.
4. Bamshad M, Jorde LB, Carey JC. A revised and extended classification of the distal arthrogryposes. Am J Med Genet 1996;65:277-81.
5. Hall JG. Arthrogryposis multiplex congenita: Etiology, genetics, classification, diagnostic approach, and general aspects. J Pediatr Orthop B 1997;6:159-66.
6. Stilli S, Antonioli D, Lampasi M, Donzelli O. Management of hip contractures and dislocations in arthrogryposis. Musculoskelet Surg 2012;96:17-21.
7. Gruel CR, Birch JG, Roach JW, Herring JA. Teratologic dislocation of the hip. J Pediatr Orthop 1986;6:693-702.
8. Hass J. Congenital Dislocation of the Hip. Illinois: Charles C Thomas Publisher; 1951.
9. Akazawa H, Oda K, Mitani S, Yoshitaka T, Asaumi K, Inoue H. Surgical management of hip dislocation in children with arthrogryposis multiplex congenita. J Bone Joint Surg Br 1998;80:636-40.
10. Horton WA, Rimoin DL, Lachman RS, Skovby F, Hollister DW, Spranger J, et al. The phenotypic variability of diastrophic dysplasia. J Pediatr 1978;93:609-13.
11. Coleman SS. Teratologic congenital dislocation. In: Congenital Dysplasia and Dislocation of the Hip. St. Louis, MO: CV Mosby; 1978. p. 249-56.
12. Friedlander HL, Westin GW, Wood WL Jr. Arthrogryposis multiplex congenita: A review of forty-five cases. J Bone Joint Surg Am 1968;50:89-112.
13. Gibson DA, Urs ND. Arthrogryposis multiplex congenita. J Bone Joint Surg Br 1970;52:483-93.
14. Drummond DS, Mackenzie DA. Scoliosis in arthrogryposis multiplex congenita. Spine (Phila Pa 1976) 1978;3:146-51.
15. Bernstein RM. Arthrogryposis and amyoplasia. J Am Acad Orthop Surg 2002;10:417-24.
16. Lloyd-Roberts GC, Lettin AW. Arthrogryposis multiplex congenita. J Bone Joint Surg Br 1970;52:494-508.
17. Staheli LT, Chew DE, Elliott JS, Mosca VS. Management of hip dislocations in children with arthrogryposis. J Pediatr Orthop 1987;7:681-5.
18. St Clair HS, Zimbler S. A plan of management and treatment results in the arthrogrypotic hip. Clin Orthop Relat Res 1985;194:74-80.
19. Huurman WW, Jacobsen ST. The hip in arthrogryposis multiplex congenita. Clin Orthop Relat Res 1985;194:81-6.
20. Williams P. The management of arthrogryposis. Orthop Clin North Am 1978;9:67-88.
21. Martin S, Tobias JD. Perioperative care of the child with arthrogryposis. Paediatr Anaesth 2006;16:31-7.
22. Bevan WP, Hall JG, Bamshad M, Staheli LT, Jaffe KM, Song K. Arthrogryposis multiplex congenita (amyoplasia): An orthopaedic perspective. J Pediatr Orthop 2007;27:594-600.


How to Cite this Article: Dey S, Gogoi P, Gogoi R, Ahmed T, Patel R, Phukan D | Teratologic Hip Dislocations: Controversies and Consensus | International Journal of Paediatric Orthopaedics | May-August 2020; 6(2): 33-38.

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