Tag Archive for: Limb Lengthening

Management of Limb Deformities in Skeletal Dysplasia

Volume 11 | Issue 1 | Januar-April 2025 | Page: 44-50 | Binu T Kurian, Aditi Pinto, James A Fernandes

DOI- https://doi.org/10.13107/ijpo.2025.v11.i01.222

Open Access License: CC BY-NC 4.0

Copyright Statement: Copyright © 2025; The Author(s).

Submitted: 29/01/2025; Reviewed: 22/02/2025; Accepted: 17/03/2025; Published: 10/04/2025

Authors: Binu T Kurian MS Ortho [1], Aditi Pinto MS Ortho [1], James A Fernandes FRCS Tr & Ortho [2]

[1] Department of Orthopaedics, St. John’s Medical College, Hospital, Bangalore, Karnataka, India.
[2] Department of Orthopaedics, Sheffield Children’s Hospital NHS Trust Sheffield S10 4 NH United Kingdom

Address of Correspondence

Dr. Binu T Kurian,
Department of Orthopaedics St. John’s Medical College, Hospital, Bangalore, Karnataka, India.
E-mail: binu.k@stjohns.in

Abstract

Skeletal Dysplasia encompasses a diverse group of genetic conditions that predominantly affect bone and cartilage formation. The clinical assessment of these conditions requires a detailed family history to assess the genetic inheritance patterns and physical examination of the limb length discrepancies, joint laxity, spinal alignment, and gait abnormalities to identify deviations from normal skeletal development. Pharmacological therapy consists of Bisphosphonates to improve the bone density in conditions like osteogenesis imperfecta. Surgical procedures include Growth modulation techniques, limb lengthening procedures, corrective osteotomies and joint reconstructions. A Detailed genetic counselling is key to parents with a history of skeletal dysplasia in the family to assess recurrence risks, explore reproductive options, and guide personalized treatment strategies. With advancements in gene therapy, 3D navigation and patient specific implants and prosthesis there is a promising future in the management of limb deformities in Skeletal dysplasia
Keywords: Skeletal Dysplasia, Lower limb deformity, Guided Growth, Limb Lengthening

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How to Cite this Article:  Kurian BT, Pinto A, Fernandes JA. Management of Limb Deformities in Skeletal Dysplasia. International Journal of Paediatric Orthopaedics. January-April 2025; 11(1): 44-50 .

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Basics of Paediatric Limb Reconstruction Surgeries

Volume 10 | Issue 2 | May-August 2024 | Page: 2-11 | Prateek Rastogi, Nitish Arora, Yogesh Patel 

DOI- https://doi.org/10.13107/ijpo.2024.v10.i02.182

Submitted: 18/05/2024; Reviewed: 14/06/2024; Accepted: 19/07/2024; Published: 10/08/2024

Authors: Prateek Rastogi MS Ortho [1], Nitish Arora MS Ortho [2], Yogesh Patel MS Ortho [3]

[1] Department of Orthopaedics, Sharda Hospital, Greater Noida, Uttar Pradesh, India.
[2] Department of Orthopaedics, Medicover Hospital, Khargar, Navi Mumbai, Maharashtra, India.
[3] Department of Orthopaedics, Sagar Multispeciality Hospital, Bhopal, Madhya Pradesh, India.

Address of Correspondence

Dr. Prateek Rastogi,
Paediatric Orthopaedics and Limb Reconstruction Surgeon, Department of Orthopaedics, Sharda Hospital, Greater Noida, Uttar Pradesh, India.
E-mail: prateek.rastogi12@gmail.com

Abstract

Paediatric limb reconstruction surgeries play a pivotal role in managing congenital and acquired deformities, limb length discrepancies, and complex musculoskeletal disorders in children. These procedures aim to restore alignment, function, and length while preserving growth potential and minimizing long-term disability. Unlike adult cases, paediatric reconstructions demand unique considerations due to ongoing skeletal development, necessitating precise planning to avoid growth plate damage. This review outlines the evolving indications for reconstruction—including congenital conditions like various hemimelia and bony deficiency, as well as acquired deformities from trauma, infection, and tumors. Foundational principles such as anatomical and mechanical axes and their deviation, CORA (Center of Rotation of Angulation), and ACA (Angulation Correction Axis) are discussed alongside osteotomy planning and execution. Techniques of gradual deformity correction such as growth modulation, and distraction osteogenesis are examined in depth, highlighting the roles of devices like Ilizarov fixators, hexapods, and intramedullary lengthening nails. Recent advancements in imaging, surgical planning, and implant design have significantly improved outcomes, although complications such as joint stiffness, infection, and secondary deformities persist. With increasing precision and a growing array of tools, paediatric limb reconstruction continues to evolve, offering promising outcomes and functional restoration to affected children.
Keywords: Paediatric limb reconstruction, Deformity Correction, Limb Lengthening, Growth Modulation, Distraction Osteogenesis, Osteotomy Techniques

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How to Cite this Article:  Rastogi P, Arora N, Patel Y| Basics of Paediatric Limb Reconstruction Surgeries| International Journal of Paediatric Orthopaedics | May-August 2024; 10(2): 02-11. https://doi.org/10.13107/ijpo.2024.v10.i02.182

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