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The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review

Volume 4 | Issue 2 | July-December 2018 | Page: 27-31 | Nada Garrouche, Saida Jerbi, Nedra Chouchane, Wassia Kessomtini, Hssine Hamza DOI- 10.13107/ijpo.2018.v04i02.015 Authors: Nada Garrouche, Saida Jerbi, Nedra Chouchane, Wassia Kessomtini [1], Hssine Hamza Departments of Radiology and, [1] Physical Medicine Rehabilitation, Taher Sfar University Hospital, Mahdia- Tunisia Address of Correspondence Dr. Nada […]

Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb

Volume 4 | Issue 2 | July-December 2018 | Page: 20-26 | Brigid M. Aherne, Fergal P. Monsell DOI- 10.13107/ijpo.2018.v04i02.014 Authors: Brigid M. Aherne, Fergal P. Monsell [1] Medical Student, University of Bristol, [1] Consultant Orthopaedic Surgeon, Bristol Royal Hospital for Children, Bristol, England, United Kingdom. Address of Correspondence Mr. Fergal P. Monsell, Bristol […]

The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review

Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb

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The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review

Volume 4 | Issue 2 | July-December 2018 | Page: 27-31 | Nada Garrouche, Saida Jerbi, Nedra Chouchane, Wassia Kessomtini, Hssine Hamza

DOI- 10.13107/ijpo.2018.v04i02.015

Authors: Nada Garrouche, Saida Jerbi, Nedra Chouchane, Wassia Kessomtini [1], Hssine Hamza

Departments of Radiology and, [1] Physical Medicine Rehabilitation, Taher Sfar University Hospital, Mahdia- Tunisia

Address of Correspondence
Dr. Nada Garrouche,
Rue Habib Zine el Abidine n°200 (7) Sahloul 2 Sousse 4054-Tunisia.
E-mail: nadagarrouche@yahoo.fr

Abstract

Sprengel’s deformity is the congenital failure of descent of the scapula. The diagnosis is based on a clinical examination and radiological procedures. Volume rendering three-dimensional computed tomography reconstructions analyze the precise topography and spatial proportions of examined bone structures. It enables an optional rotation of visualized bone structures to clarify the anatomical abnormalities. Ultrasound and magnetic resonance are useful in prenatal management and for the diagnosis of concomitant abnormalities. In this paper, we report our imaging experience from one child with Sprengel’s deformity and discuss the importance of imaging techniques with a particular focus on the role of three-dimensional reconstructions.
Keywords: Congenital high scapula, CT, MRI, Sprengel’s deformity, ultrasound, volume rendering 3D-CT

References

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How to Cite this Article: Garrouche N, Jerbi S, Chouchane N, Kessomtini W, Hamza H The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review | July-December 2018; 4(2): 27-31.

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Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb

Volume 4 | Issue 2 | July-December 2018 | Page: 20-26 | Brigid M. Aherne, Fergal P. Monsell

DOI- 10.13107/ijpo.2018.v04i02.014

Authors: Brigid M. Aherne, Fergal P. Monsell [1]

Medical Student, University of Bristol, [1] Consultant Orthopaedic Surgeon, Bristol Royal Hospital for Children, Bristol, England, United Kingdom.

Address of Correspondence
Mr. Fergal P. Monsell,
Bristol Royal Hospital for Children, Upper Maudlin St, Bristol BS2 8BJ, England, United Kingdom.
E-mail: Fergal.Monsell@UHBristol.nhs.uk

Abstract

Background: Meningococcal septicaemia is a potentially life-threatening disease and remains the most common infective cause of mortality in the UK. Improvements in healthcare have led to early recognition and treatment, and a decrease in mortality. As more children now survive the initial acute illness, the long-term musculoskeletal consequences have become more prevalent. These include growth plate injury, tissue loss and amputation. Patients with limb loss present specific difficulties due to the effect of remaining longitudinal growth on the function of the residual limb, and often require surgical treatment that continues throughout childhood.
Patients and Methods: This case series reviews the histories of 13 children who underwent amputation as a complication of meningococcal septicaemia. All patients attend a specialist clinic and our experience in the management of the residual limb is described.
Results: Thirteen patients, with a mean age of 16 months at the onset of meningococcal septicaemia, required amputation in the management of the skeletal consequences of the infection. Revision surgery was necessary for all 13 patients and involved management of bone overgrowth, growth arrest, scar and soft tissue contracture, neuroma development, and infection. The details of our approach to each of these complications is described.
Conclusion: Due to improvements in diagnosis and initial management, a significant proportion of patients are surviving infantile meningococcal septicaemia. Many develop musculoskeletal consequences including amputation, and this case series serves to increase knowledge in the complex managements of the residual limb in these patients.
Keywords: Amputation, meningococcal septicaemia, residual limb

References

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How to Cite this Article: Aherne BM, Monsell FP | Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb | July-December 2018; 4(2): 20-26.

Half Sized Blog Element (Single Author Style)

Half Sized Blog Element (Multi Author Style)

The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review

Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb

The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review

Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb

Full Sized Blog Element (Big Preview Pic)

The Role of Imaging in Diagnosis and Management of Congenital High Scapula (Sprengel’s Deformity): Case Report and Review

Authors: Nada Garrouche, Saida Jerbi, Nedra Chouchane, Wassia Kessomtini [1], Hssine Hamza

Abstract

References

(Article Text HTML) (Download PDF)

Amputation Following Meningococcal Septicaemia in Children: the Surgical Management of the Residual Limb

Authors: Brigid M. Aherne, Fergal P. Monsell [1]

Abstract

References

(Article Text HTML) (Download PDF)

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