Tag Archive for: Deformity correction

Management of Limb Deficiencies

Volume 10 | Issue 2 | May-August 2024 | Page: 48-54 | Sakti Prasad Das, Sankar Ganesh, Prateek Behera

DOI- https://doi.org/10.13107/ijpo.2024.v10.i02.194

Submitted: 11/03/2024; Reviewed: 08/04/2024; Accepted: 25/06/2024; Published: 10/08/2024


Authors: Sakti Prasad Das MS(Ortho.), DNB(PMR) [1], Sankar Ganesh MPT [2], Prateek Behera MS(Ortho.), DNB(Ortho.) [3]

[1] Medical Education & Training, DRIEMS University, Odisha, Tangi, Cuttack, Odisha, India.
[2] Department of Physiotherapy, Composite Regional Centre, Lucknow, Uttar Pradesh, India.
[3] Department of Orthopaedics, AIIMS Bhopal, Madhya Pradesh, India.

Address of Correspondence

Dr. Sakti Prasad Das,
Director, Medical Education & Training, DRIEMS University, Odisha, Tangi, Cuttack, Odisha, India.
E-mail: sakti2663@yahoo.com


Abstract

Limb deficiency disorders encompass a wide variety of congenital anomalies that have a significant underdevelopment or even complete absence of bones in the limbs. Treatment of these conditions must be holistic with the child at the centre. This article provides a review of the current understanding of the management of such conditions. Surgical treatment offers a practical and effective solution for treating many variants of congenital limb abnormalities. Although novel surgical treatments may expand the range of disorders that can be treated, it is crucial for both the surgeon and the family to be aware of the careful prognosis associated with the methods used. Additionally, the importance of an amputation as an option should always be kept under consideration.
Keywords: Amputation, Congenital Abnormalities, Deformity correction, Limb reconstruction, Pediatric skeletal deficiencies, Skeletal dysplasia


References

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How to Cite this Article:  Das SP, Ganesh S, Behera P | Management of Limb Deficiencies | International Journal of Paediatric Orthopaedics | May-August 2024; 10(2): 48-54. https://doi.org/10.13107/ijpo.2024.v10.i02.194

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Basics of Paediatric Limb Reconstruction Surgeries

Volume 10 | Issue 2 | May-August 2024 | Page: 2-11 | Prateek Rastogi, Nitish Arora, Yogesh Patel 

DOI- https://doi.org/10.13107/ijpo.2024.v10.i02.182

Submitted: 18/05/2024; Reviewed: 14/06/2024; Accepted: 19/07/2024; Published: 10/08/2024


Authors: Prateek Rastogi MS Ortho [1], Nitish Arora MS Ortho [2], Yogesh Patel MS Ortho [3]

[1] Department of Orthopaedics, Sharda Hospital, Greater Noida, Uttar Pradesh, India.
[2] Department of Orthopaedics, Medicover Hospital, Khargar, Navi Mumbai, Maharashtra, India.
[3] Department of Orthopaedics, Sagar Multispeciality Hospital, Bhopal, Madhya Pradesh, India.

Address of Correspondence

Dr. Prateek Rastogi,
Paediatric Orthopaedics and Limb Reconstruction Surgeon, Department of Orthopaedics, Sharda Hospital, Greater Noida, Uttar Pradesh, India.
E-mail: prateek.rastogi12@gmail.com


Abstract

Paediatric limb reconstruction surgeries play a pivotal role in managing congenital and acquired deformities, limb length discrepancies, and complex musculoskeletal disorders in children. These procedures aim to restore alignment, function, and length while preserving growth potential and minimizing long-term disability. Unlike adult cases, paediatric reconstructions demand unique considerations due to ongoing skeletal development, necessitating precise planning to avoid growth plate damage. This review outlines the evolving indications for reconstruction—including congenital conditions like various hemimelia and bony deficiency, as well as acquired deformities from trauma, infection, and tumors. Foundational principles such as anatomical and mechanical axes and their deviation, CORA (Center of Rotation of Angulation), and ACA (Angulation Correction Axis) are discussed alongside osteotomy planning and execution. Techniques of gradual deformity correction such as growth modulation, and distraction osteogenesis are examined in depth, highlighting the roles of devices like Ilizarov fixators, hexapods, and intramedullary lengthening nails. Recent advancements in imaging, surgical planning, and implant design have significantly improved outcomes, although complications such as joint stiffness, infection, and secondary deformities persist. With increasing precision and a growing array of tools, paediatric limb reconstruction continues to evolve, offering promising outcomes and functional restoration to affected children.
Keywords: Paediatric limb reconstruction, Deformity Correction, Limb Lengthening, Growth Modulation, Distraction Osteogenesis, Osteotomy Techniques


References

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How to Cite this Article:  Rastogi P, Arora N, Patel Y| Basics of Paediatric Limb Reconstruction Surgeries| International Journal of Paediatric Orthopaedics | May-August 2024; 10(2): 02-11. https://doi.org/10.13107/ijpo.2024.v10.i02.182

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