Tag Archive for: scoliosis

Management of Paediatric Spinal Pathologies in Skeletal Dysplasia

Volume 11 | Issue 1 | Januar-April 2025 | Page: 17-24 | Arjun Dhawale, Bhushan Sagade, Atif Naseem, Abhay Nene

DOI- https://doi.org/10.13107/ijpo.2025.v11.i01.216

Open Access License: CC BY-NC 4.0

Copyright Statement: Copyright © 2025; The Author(s).

Submitted: 29/01/2025; Reviewed: 13/02/2025; Accepted: 08/03/2025; Published: 10/04/2025

Authors: Arjun Dhawale MS Ortho [1, 2], Bhushan Sagade MS Ortho [1], Atif Naseem MS Ortho [1], Abhay Nene MS Ortho [1, 2]

[1] Department of Orthopaedics, B.J. Wadia Hospital for Children, Parel, Mumbai, Maharashtra, India.
[2] Department of Orthopaedics, Sir H.N. Reliance Foundation Hospital, Girgaon, Mumbai, Maharashtra, India.

Address of Correspondence

Dr. Arjun Dhawale,
Department of Orthopaedics , B.J. Wadia Hospital For Children, Parel, Mumbai 400012, Maharashtra, India.
E-mail: arjundhawale@hotmail.com

Abstract

Treatment of spinal deformities in skeletal dysplasia is challenging. There should be a low threshold for imaging the cervical spine for instability at the craniovertebral junction. A thorough evaluation by a multidisciplinary is necessary before deciding upon any surgery. Deformity, spinal stenosis, and neurological deficit can occur. Medical optimization should be considered. Treatment should be tailored to each patient based on the symptoms, signs, the curve magnitude, and overall prognosis of survival in these patients. Implant failure, intraoperative neuromonitoring signal alerts, and junctional kyphosis are common complications . Most literature is based on expert consensus and small series, there are few long-term outcomes studies.
Keywords: Kyphosis, Scoliosis, Craniovertebral instability, Skeletal Dysplasia, Spinal Fusion, Achondroplasia, Mucopolysaccharidosis

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How to Cite this Article:  Dhawale A, Sagade B, Naseem A, Abhay Nene A. Management of Paediatric Spinal Pathologies in Skeletal Dysplasia. International Journal of Paediatric Orthopaedics. January-April 2025; 11(1): 17-24.

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Assessment in adolescent scoliosis

Volume 6 | Issue 1 | Jan – April 2020 | Page 2-6 |  Connor J. S. McKee.

Authors : Connor J. S. McKee [1]

[1] Royal Victoria Hospital, 274 Grosvenor Rd, Belfast BT12 6BA, Belfast, Northern Ireland.

Address of Correspondence
Dr. Connor J. S. McKee,
Royal Victoria Hospital, 274 Grosvenor Rd, Belfast BT12 6BA, Belfast, Northern Ireland.
E-mail: connor.mckee@ntlworld.com,
cmckee43@qub.ac.uk

Abstract

Background: Adolescent idiopathic scoliosis is associated with lateral spinal curvature, vertebral rotation and rib cage distortion which disrupts normal, symmetrical thoracic movement leading to restriction of lung expansion and impaired pulmonary function. The effects of scoliosis on lung growth, airway function and exercise capacity are well documented but it is unclear how altered rib positioning affects lung function. This paper compares two different radiological measurements with pulmonary function.
Methods: The study compared two measures of deformity: Cobb angle and average rib-vertebral angle difference with pulmonary functioning. Existing literature describes Cobb angle as a useful indicator of pulmonary dysfunction. However, there are few reports on the use of rib-vertebral angle difference and these are limited to a single measurement taken at the apical vertebrae. This study of 53 patients used an average rib-vertebral angle difference over five vertebral levels. This measure gives a more representative measurement of the scoliotic deformity. This measure was then correlated with the patient’s Cobb angle and pulmonary function.
Results: Using Spearman’s rank correlation coefficient, average rib-vertebral angle difference correlated strongly with Cobb angle (0.83), forced vital capacity (-0.81), forced expiratory volume in 1 second (-0.76), and peak expiratory flow (-0.60).
Conclusions: The study found that measurement of Cobb angle is superior to average rib-vertebral angle difference across five vertebral levels.
Keywords: Idiopathic, scoliosis, RVAD, Cobb, measurement.
Study design: Retrospective correlation of pre-operative pulmonary function tests and radiological measurements

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How to Cite this Article: McKee C J S Assessment in adolescent | scoliosis | International Journal of
Paediatric Orthopaedics | Jan-April 2020; 6(1):- .

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