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The Hip in Skeletal Dysplasia: Evaluation & Management

Volume 11 | Issue 1 | Januar-April 2025 | Page: 29-38 | Gaurav Gupta, Easwar T R, Hitesh Shah, Mohan V Belthur DOI- https://doi.org/10.13107/ijpo.2025.v11.i01.220 Open Access License: CC BY-NC 4.0 Copyright Statement: Copyright © 2024; The Author(s). Submitted: 13/01/2025; Reviewed: 08/02/2025; Accepted: 15/03/2025; Published: 10/04/2025 Authors: Gaurav Gupta MS Ortho [1], Easwar T R MS […]

A Case of Osteofibrous Dysplasia Treated with a Hybrid Approach: Clinical and Radiological Outcomes

Volume 10 | Issue 3 | September-December 2024 | Page: 33-38 | Vivek Madankar, K. Ramkumar Reddy, Roshan Kumar Mohanty DOI- https://doi.org/10.13107/ijpo.2024.v10.i03.208 Open Access License: CC BY-NC 4.0 Copyright Statement: Copyright © 2024; The Author(s). Submitted: 15/11/2024; Reviewed: 22/11/2024; Accepted: 01/12/2024; Published: 10/12/2024 Authors: Vivek Madankar MS Ortho [1], K. Ramkumar Reddy MS Ortho [1], […]

The Hip in Skeletal Dysplasia: Evaluation & Management

A Case of Osteofibrous Dysplasia Treated with a Hybrid Approach: Clinical and Radiological Outcomes

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The Hip in Skeletal Dysplasia: Evaluation & Management

Volume 11 | Issue 1 | Januar-April 2025 | Page: 29-38 | Gaurav Gupta, Easwar T R, Hitesh Shah, Mohan V Belthur

DOI- https://doi.org/10.13107/ijpo.2025.v11.i01.220

Open Access License: CC BY-NC 4.0

Submitted: 13/01/2025; Reviewed: 08/02/2025; Accepted: 15/03/2025; Published: 10/04/2025

Authors: Gaurav Gupta MS Ortho [1], Easwar T R MS Ortho [2], Hitesh Shah MS Ortho [3], Mohan V Belthur MS Ortho, FRCS (Tr & Orth), FRCSC [4, 5]

[1] Department of Orthopaedics, Child Ortho Clinic, Delhi-NCR, India.
[2] Department of Orthopaedics, Baby Memorial Hospital, Kozhikode, Kerala, India.
[3] Department of Orthopaedics, Kasturba Medical College, Manipal, Karnataka, India.
[4] Department of Orthopaedics, Phoenix Children’s Hospital, Phoenix, Arizona, USA.
[5] Department of Child Health & Orthopaedics, University of Arizona College of Medicine – Phoenix.

Address of Correspondence

Dr Mohan Belthur,
MD, FRCS (Tr & Orth), FRCSC
Department of Child Health & Orthopaedics, University of Arizona College of Medicine – Phoenix.
Director, Paediatric Limb Reconstruction Services
Co-Director, Neuroorthopaedic Services
Co-Director, Bubba Watson & Ping Motion Analysis Laboratory
Department of Orthopaedics, Phoenix Children’s Hospital, Phoenix, Arizona, USA.

Abstract

Skeletal dysplasias represent a heterogeneous group of over 500 genetic disorders affecting the growth, development, and structural integrity of bone and cartilage. Hip deformities in skeletal dysplasia (S.D) represent a significant challenge in pediatric orthopaedic practice. They significantly impact mobility and quality of life in children with S.D. Despite advances in surgical techniques and implant technology, patients with skeletal dysplasia continue to face higher complication rates and more challenging management decisions.
Early identification and intervention can prevent progressive deformity and secondary complications. A multidisciplinary approach combining careful preoperative planning, specialised surgical techniques, and dedicated rehabilitation protocols offers the best opportunity to optimise outcome.
Keywords: Skeletal Dysplasia, Hip deformities, Natural History, Management, Outcomes.

References

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How to Cite this Article: Gupta G, TR Easwar, Shah H, Belthur MV | The Hip in Skeletal Dysplasia: Evaluation & Management | International Journal of Paediatric Orthopaedics | January-April 2025; 11(1): 29-38

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A Case of Osteofibrous Dysplasia Treated with a Hybrid Approach: Clinical and Radiological Outcomes

Volume 10 | Issue 3 | September-December 2024 | Page: 33-38 | Vivek Madankar, K. Ramkumar Reddy, Roshan Kumar Mohanty

DOI- https://doi.org/10.13107/ijpo.2024.v10.i03.208

Open Access License: CC BY-NC 4.0

Submitted: 15/11/2024; Reviewed: 22/11/2024; Accepted: 01/12/2024; Published: 10/12/2024

Authors: Vivek Madankar MS Ortho [1], K. Ramkumar Reddy MS Ortho [1], Roshan Kumar Mohanty MS Ortho [1]

[1] Department of Orthopaedics, Kakatiya Medical College, Warangal, Telangana, India.

Address of Correspondence

Dr. Vivek Madankar,
Department of Orthopaedics, Kakatiya Medical College, Warangal, Telangana, India.
E-mail: vivekmadankar@gmail.com

Abstract

Introduction: Osteofibrous dysplasia (OFD) is a rare, benign, and self-limiting fibro-osseous lesion primarily affecting the cortical bone of the tibia and fibula in children and adolescents. OFD presents diagnostic challenges due to its clinical and radiological resemblance to adamantinoma, a malignant bone tumor. Accurate diagnosis and appropriate treatment are essential to prevent complications and recurrence.
Case Report: We report the case of an 11-year-old boy with a four-month history of pain and a longstanding swelling in his right tibia. Clinical examination revealed a firm, well-circumscribed lesion in the tibial cortex. Imaging demonstrated a mixed sclerotic and lytic lesion with characteristic features, including a multilocular “soap bubble” appearance. Histopathological evaluation confirmed the diagnosis of OFD. The patient underwent a hybrid treatment approach involving surgical excision sparing the posterior cortex, followed by functional cast bracing. This strategy facilitated early mobilization and complete recovery. Radiological evaluation at six weeks demonstrated neo-osteogenesis, with full bone healing achieved by 12 weeks. At the two-year follow-up, the patient exhibited full functional recovery with no signs of recurrence.
Conclusion: This case highlights the successful management of OFD using a hybrid surgical and non-surgical approach, emphasizing the importance of accurate diagnosis and tailored treatment strategies. Combining surgical resection with functional bracing allowed for effective management, early weight-bearing, and prevention of complications. This approach adds to the orthopedic literature by illustrating an alternative, cost-effective treatment protocol for this rare bone disorder.
Keywords: Osteofibrous dysplasia, Tibial lesion, Hybrid treatment, Surgical excision, Functional cast bracing, Pediatric orthopedics

References

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How to Cite this Article: Madankar V, Reddy KR, Kumar R | A Case of Osteofibrous Dysplasia Treated with a Hybrid Approach: Clinical and Radiological Outcomes | International Journal of Paediatric Orthopaedics | September-December 2024; 10(3): 33-38.

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